How should phenylketonuria patients eat

1. The diet of children with phenylketonuria has special requirements for protein

--Because phenylalanine mostly exists maternal pku in various proteins, children with phenylketonuria have a very special requirement for protein. The demand for other related nutrients: sugar, fat, vitamins and minerals (including trace metal elements) is the same as the development of children with general education;

2. Low phenylalanine diet should be adopted

--It is not enough to eat ordinary food completely. We must eat some special phenylalanine free (or low) protein, which is artificially made and belongs to a specially developed special nutritional food; Secondly, children with phenylketonuria should also eat enough protein, otherwise it will affect growth and development.

3. Special nutritional food

--In order to grow and develop, 80% of the protein necessary every day is supplied by special nutritious foods made manually. Such foods include:

1) No (or low) phenylalanine nutritional powder - commonly known as milk powder;

2) No (or low) phenylalanine passes through protein powder;

3) Phenylketonuria special low phenylalanine staple food - such as staple meal, flour, dumpling powder, self hair powder, starch rice, etc. Because rice, as a flour food for the treatment of children with phenylketonuria, also belongs to "high" phenylalanine food;

4. The remaining 20% uses natural protein sources

--To select and provide high-quality structural proteins, such as meat, eggs and fish, the content of amino acids in their proteins must be adjusted, which is more suitable for human use;

5. Low phenylalanine diet is convenient when using the above special foods.

maternal pku

2、 What food can children with phenylketonuria eat in addition to the above special food

There are many foods to eat, such as:

1. Starchy food

——Vermicelli, vermicelli, jelly, lotus, lotus root powder, horseshoe, potato, yam, sweet potato, cassava, taro, pumpkin, etc.;

2. Sugars

--White sugar, glucose, fructose, lactose, maltose, etc;

3. Fat

Various vegetable oils (peanut oil, soybean oil, rapeseed oil, sunflower seed oil, sesame oil, olive oil, coconut oil, medium chain fatty acid (MCT), etc.).

4. Animals that remove oil residue after refining

- pigs, cattle, sheep, chickens, ducks, goose oil, butter, artificial vegetable butter and so on;

5. Low phenylalanine food

Fruits and vegetables (Note: plant beans, such as kidney beans, cowpeas, beans, mung beans, cloud beans, etc., cannot be eaten).